Keywords
dysparathyroidism
intracerebral calcifications
parkinsonism Introduction âgée
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Abstract
Introduction :
Fahr's syndrome is a rare anatomoclinical entity, associating a calcification of the basal ganglia symmetrically with a very varied neuropsychiatric picture. It is most often diagnosed at a young age. The objective of this study was to report a case of Fahr syndrome revealed by parkinsonian manifestations.
Observation :
We report the case of a 73-year-old patient received for consultation on suspicion of Parkinson's disease. The brain scan showed bilateral and symmetrical calcifications of the basal ganglia. The biological assessment revealed dysparathyroidism. The diagnosis of Fahr syndrome secondary to hypovitaminosis D was retained. The clinical course was favorable with vitamin-calcium supplementation.
Conclusion :
Fahr syndrome is a rare pathology. It should be considered in front of symmetrical calcifications of the gray nuclei on the tomodensitometry associated with disturbance of the phosphocalcic.
References
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